Congenital Cystic Adenomatoid Malformation (CCAM) with Two Cases Introduction

Authors

  • Farzaneh Jalali Mofid Pediatric Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran.
  • Sepideh Siadati Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Abstract:

CCAM is a rare conolition in the neonatal Period. Two babies were admitted to Mofid hospital with cyanosis and respiratory distress. Pneumectomy was done for both of them for space occupaying lesion. Pathology examination of first case showed area of cuboidal epithelium lined tubes and spaces resembling fetal bronchioles, which are torn in folds. In second case, pathologic examination revealed cystically dilated irregular stellate shaped bronchiolar structures lined by cuboidal epithelium cells and surrounded by alveolar ductuls. These malformation were not associated with other abnormalities and were type I & III respectively depending on Stocker's classification.

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Journal title

volume 22  issue 3

pages  55- 59

publication date 1998-09

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